Werlhof tus kab mob - trombocytopenic purpura - ib tug kab mob tshwm sim nyob rau hauv daim ntawv ntawm hemorrhagic effusions tawm tsam tom qab ntawm nce aggregation (gluing) ntawm platelets. Tsim microthrombi clog cov lumens ntawm cov hlab ntsha me me. Tsis tas li ntawd xwb, muaj lub siab ntawm cov qe ntshav thiab txo qis ntawm cov platelets.
Ua rau Werlhof tus kab mob
Tam sim no, qhov ua tsis ncaj rau ntawm cov kab mob trombocytopenic purpura tsis paub. Muab cov ntawv thij ob thiab theem nrab ntawm Verlhof tus kab mob. Cov ntawv xub thawj yog kev xeeb ceem nyob rau hauv los yog tshwm sim los ntawm kev kis mob. Cov ntawv theem nrab muaj cov cim qhia ntawm ntau hom kab mob.
Cov tsos mob ntawm Verlhof tus kab mob
Tus kab mob no pib acutely, vim tsis paub tias vim li cas, qee zaus tiv thaiv cov keeb kwm mob plab hnyuv lossis ARI. Hauv cov neeg mob thaum pib thawj theem, cov tsos mob tshwm sim hauv qab no pom tau tias:
- kub cev;
- xeev siab (ntuav tau);
- mob taub hau;
- kev tsis muaj zog, qaug zog;
- mob hauv siab thiab hauv plab.
Lub ntsiab lus tseem ceeb yog bruises thiab subcutaneous hemorrhages, uas piav txog lub npe thib ob ntawm tus kab mob - thrombocytopenic purpura.
Tom qab luv luv, qhov hemorrhagic syndrome tau tshwm sim tshwj xeeb hauv daim ntawv:
- qhov ntswg, qhov hnyuv taum, thiab cov poj niam kuj tau uterine;
- ntshav cov pos hniav , mucous membranes;
- hemorrhages nyob rau hauv retina ntawm lub qhov muag;
- hemoptysis.
Hemorrhagic tshwm sim yog nrog nws cov lus los ntawm kev ntshaib leeg, xws li:
- retardation;
- nkees nkees;
- disorientation nyob rau hauv qhov chaw thiab lub sijhawm;
- tsis pom kev;
- unilateral tuag tes tuag taw.
Hauv cov mob hnyav heev, nws tsim nyog los tsim lub coma.
Hemorrhages nyob rau hauv daim tawv nqaij ua ntev thiab nyob nrog ib thaj chaw loj. Nyob ntawm cov tshuaj, effusions muaj xim los ntawm xim liab-daj kom daj (zoo li cov laus laus).
Kev kuaj mob ntawm Verlhof tus kab mob pib nrog ib tus neeg mob kev xeem thiab anamnesis. Qhov kev ntsuam xyuas muaj xws li cov kev kuaj nram qab no:
- Kev ntsuam xyuas ntawm ntshav (OAK). Tus kab mob no yog txiav txim siab los ntawm kev txo cov qib erythrocytes thiab hemoglobin, txo cov platelets thiab xyuas cov antiplatelet antibodies.
- Sternary puncture - noj cov pob txha pob txha rau kev soj ntsuam los ntawm kev hnyuv tws. Hauv kev tshawb nrhiav ntawm cov kab mob ntawm tes, qhov nce hauv cov kab mob megakaryocytes, muaj tsawg tus platelets, muaj nyob, thaum tsis muaj lwm yam hloov hauv cov pob txha pob txha, piv txwv li, cov uas yog cov yam ntxwv ntawm qog formations.
- Trepanobiopsy - kev kawm txog cov pob txha pob txha nrog periosteum thiab pob txha (los ntawm thaj chaw plab zawv plawv), nrog rau kev pab los ntawm kev kho mob ntawm trephine. Nrog Verlhof tus kab mob, qhov sib piv ntawm cov rog thiab hematopoietic pob txha marrow sib raug.
Kev kho mob ntawm Verlhof tus kab mob
Kev ntsuas tshuaj nyob ntawm seb nws mob li cas. Kev kho yog ua tiav los ntawm ib txoj kev hauv qab no:
- Kev siv corticosteroids rau lub hom phiaj ntawm kev ntes cov mob hemorrhagic syndrome thiab nce qib platelets nyob rau hauv cov ntshav. Prednisalon tau sau rau ntawm tus nqi ntawm 1 mg rau 1 kg ntawm tus neeg mob hnyav ib hnub. Nyob rau hauv cov ntaub ntawv ntawm ib tug loj chav kawm ntawm tus kab mob, lub koob tshuaj yog doubled.
- Yog tias qhov zoo siv tsis tiav, tus neeg mob tau pom zoo kom tshem tus po . Raws li kev txheeb xyuas kab mob kev nkeeg, nyob rau hauv 80% ntawm cov neeg mob tom qab phais kev kho tiav tag nrho kev rov qab raug cai.
- Hauv qee zaum, tom qab tus kab mob spleenectomy spleen, ntshav los, thiab tus kab mob tseem nyob, immunosuppressants yog tus kws kho mob (Azathioprine, Vincristine) thiab glucocosteroids.
Txhawm rau tshem tawm cov tsos mob ntawm sab nraud ntawm hemorrhagic syndrome, cov neeg ua haujlwm haemostatic siv:
- Adroxon;
- Noj cov zaub mov;
- Hemostatic daim txhuam cev;
- estrogens.